Macular atrophy is relatively rare skin disease and is characterized histologically by deficiency of elastic fibers and clinically by circumscribed area of thin, wrinkled bulging out skin. Whether the association with identificable specific dermatosis or not divides the macular atrophy into primary & secondary type.
I present a case of widespreaded primary macular atrophy. A 28 year old male has been suffered from symptomless, slowly progressive, numerous, well demarcated, neither coalesced nor grouped, rice sized, round to oval shaped, hypopigmented, protruded, wrinkled surfaced eruptions which began from both flank at first about 3 years ago and then spreaded to abdomen, chest, back and all extremities except hands & feet.
General physical &- laboratory examinaions did not show distinct abnormality except skin findings.
Histopatholgical study revealed fragmentation, scantiness or disappearance of elastic fibers by means of Verhoeff-VanGieson stain and no increase of Periodic acid-Schiff stain positive material ruled out the possibility of amyloidosis.
Diagnosis was confirmed by clinical & histochemical findings.
Literature was briefly reviwed for the discussion.
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